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[Case Report] Dössekker’s atypical tuberous myxoedema, a rare variant of scleromyxoedema

In January, 2012, a previously well 49-year-old man of Sudanese descent presented with a 5 day history of progressive painful swelling of the face, particularly affecting the eyelids and periorbital tissues and hands. He took no drugs and had no allergies. He had travelled to Sudan 6 months previously but had had no known contact with tuberculosis. A presumptive diagnosis of angioedema was made but the swellings did not respond to multiple antihistamines, several doses of intramuscular adrenaline, high doses of systemic corticosteroids, and broad spectrum intravenous antibiotics.