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[Case Report] Proximal pulmonary artery stenosis: a rare manifestation of granulomatosis with polyangiitis

A 23-year-old man presented in June, 2015, with a 1-day history of acute onset progressive dyspnoea, but no cough, fever, or infective symptoms, orthopnoea, paroxysmal nocturnal dyspnoea, chest pain, or palpitations. He had been given a diagnosis of granulomatosis with polyangiitis 3 years previously after presenting with sinusitis, upper limb ischaemia, and renal impairment; a renal biopsy sample had shown focal necrotising glomerulonephritis and blood tests had shown both anti-neutrophil cytoplasmic antibody (ANCA) and anti-PR3 antibody.