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[Clinical Picture] Multiple enchondromas and skin angiomas: Maffucci syndrome

A 52-year-old man presented to our dermatology clinic for evaluation of several bluish nodules of the right hand and wrist (figure) that had gradually increased in number over the previous 31 years. The lesions were asymptomatic but had been causing the patient embarrassment and had started affecting his social interactions. No one in his family had a history of similar lesions. During adolescence he had had surgical excision of several painful enchondromas involving the proximal phalanx of the right fifth finger and three chondrosarcomas of the metacarpo-phalangeal joints of the right hand, but at the time he had no evidence of cutaneous lesions and therefore had been diagnosed as having Ollier disease (enchondromatosis).

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